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Pathways of ammonia detoxification to GLN in muscles linked to Increased intake of your BCAA and α-KG (cataplerosis) and prompt outcomes of BCAA and phenylbutyrate in subjects with liver cirrhosis or UCD. Beneficial impact of BCAA on ammonia detoxification to GLN may very well be blunted by GLN degradation to ammonia in enterocytes and kidneys. Ph